TY  - EJOU
AU  - Kocher, Neil J. 
AU  - Loloi, Justin 
AU  - Warrick, Joshua 
AU  - Burns, Amy S. 
AU  - Decter, Ross M. 

TI  - Ectopic ACTH-secreting neuroendocrine tumor: a rare etiology of a pediatric solid renal mass
T2  - Canadian Journal of Urology

PY  - 2019
VL  - 26
IS  - 5
SN  - 1488-5581

AB  - Neuroendocrine tumors (NETs) are rare tumors with 
varying clinical presentations. We describe the case of an 
11-year-old female presenting with Cushingoid features 
in the setting of a left-sided flank mass. Her presentation 
and evaluation suggested a paraneoplastic ectopic ACTH syndrome. She underwent open left radical nephrectomy 
and final pathology confirming a high-grade NET with 
nodal metastasis. Although exceedingly rare, ACTH-secreting tumors of the kidney can cause significant 
morbidity and mortality and so we recommend it be 
included in the differential diagnosis of pediatric renal 
masses.
KW  - pediatric
KW  -  neuroendocrine
KW  -  ACTH
KW  -  tumor; ectopic

DO  -