TY  - EJOU
AU  - Stieglitz, Lael 
AU  - Jr., Vernon M. Pais 

TI  - Implications of Erdheim-Chester disease and percutaneous renal access
T2  - Canadian Journal of Urology

PY  - 2020
VL  - 27
IS  - 6
SN  - 1488-5581

AB  - Erdheim-Chester disease (ECD) is a rare systemic 
histiocytosis with urologic manifestations in a majority 
of affected patients. An important manifestation is a 
pronounced retroperitoneal fibrosis with reported dense 
inflammatory rind surrounding the kidneys. We report a case of a patient with large stone burden necessitating 
percutaneous nephrolithotomy and the implications 
related to his Erdheim-Chester-related retroperitoneal 
fibrotic changes. Foreknowledge of these implications may 
inform perioperative counseling and surgical planning to 
maximize opportunity for successful outcomes.
KW  - nephrolithiasis
KW  -  retroperitoneal fibrosis
KW  -  Erdheim-Chester disease
KW  -  histiocytosis

DO  -