@Article{,
AUTHOR = {Lianne M. Geerdink, Gideon J. du Marchie Sarvaas, Irene M. Kuipers, Willem A. Helbing, Tammo Delhaas, Henriette ter Heide, Lieke Rozendaal, Chris L. de Korte, Sandeep K. Singh, Tjark Ebels, Mark G. Hazekamp, Felix Haas, Ad J. J. C. Bogers, Livia Kapusta},
TITLE = {Surgical outcome in pediatric patients with Ebstein’s anomaly: A multicenter, long-term study},
JOURNAL = {Structural and Congenital Heart Disease},
VOLUME = {12},
YEAR = {2017},
NUMBER = {1},
PAGES = {32--39},
URL = {http://www.techscience.com/schd/v12n1/38722},
ISSN = {3071-1738},
ABSTRACT = {<b>Objective:</b> Surgical outcomes of pediatric patients with Ebstein’s anomaly are often described as
part of all-age-inclusive series. Our objective is to focus on patients treated surgically in childhood
(0-18 y). We study the intended treatment (biventricular or 1.5 ventricle repair or univentricular
palliation), freedom from unplanned reoperation and survival of this specific age group, in a nationwide study.<br/>
<b>Design:</b> Records of all Ebstein’s anomaly patients born between 1980 and 2013 were reviewed.
Demographic variables, intraoperative procedures and postoperative outcomes were analyzed.<br/>
<b>Results:</b> Sixty-three patients underwent 109 operations. Median follow-up after diagnosis was
121 months (range 0-216 months). Twenty-nine (46%) patients required surgery in the first year
of life, including 21 who required neonatal surgery. The intended treatment was biventricular
(n = 37, 59%) and 1.5 ventricle (n = 5, 8%) repair or univentricular (n = 21, 33%) palliation. The
one-, five-, and 10-year freedom from unplanned reoperation was 89%, 79%, and 75% respectively. There were nine (14%) in hospital deaths (within 30 d after surgery). Causes of death were
low cardiac output syndrome, cardiac failure, hypoxemia, pulmonary hypertension or an unknown
cause. There were no late deaths.<br/>
<b>Conclusions:</b> Surgery in childhood represents the worse spectrum of disease, biventricular repair
is often not applied. Patients often face revision surgery. Mortality is limited to the immediate
postsurgical period.},
DOI = {}
}