@Article{chd.12623,
AUTHOR = {William N. Evans, Ruben J. Acherman, Dean Berthoty, Gary A. Mayman, Michael L. Ciccolo, Sergio A. Carrillo, Humberto Restrepo},
TITLE = {Right aortic arch with situs solitus},
JOURNAL = {Structural and Congenital Heart Disease},
VOLUME = {13},
YEAR = {2018},
NUMBER = {4},
PAGES = {624--627},
URL = {http://www.techscience.com/schd/v13n4/39037},
ISSN = {3071-1738},
ABSTRACT = {<b>Patients:</b> We reviewed all patients evaluated at our center with situs solitus, levocardia, and a right
aortic arch that were born between January 2000 and January 2018. <b>Results:</b> From our databases,
we identified 204 patients. We excluded patients with a double aortic arch from analysis. Of the
204 patients, 103 (50%) were male. Of the 204 patients, 95 (47%) had an isolated right aortic arch.
Of the 95 with an isolated right aortic arch, 4 (4%) had chromosome 22q11.2 deletion syndrome,
and 89 (94%) had a vascular ring. Of the 204 patients, 109 (53%) had a surgical intracardiac malformation. Of the 109, with an associated surgical intracardiac malformation, 38 (35%) had
chromosome 22q11.2 deletion syndrome, and 28 (26%) had a vascular ring. Overall, of the 204
patients, 200 (98%) had a vascular ring, an associated intracardiac malformation, or both. Prenatal
detection was 85% (40/47) for the subset of patients born in Southern Nevada between January
2015 and January 2018. <b>Conclusion:</b> this review, to best of our knowledge, reports one of largest
series of right aortic arches in the literature. Data from our cohort demonstrates that a right aortic
arch in situs solitus is almost always associated with pathology. Further, our center’s right aortic
arch prenatal detection rate exceeds previous reports.},
DOI = {10.1111/chd.12623}
}