TY  - EJOU
AU  - Hong, Hao 
AU  - Dong, Nianguo 
AU  - Xie, Mingxing 
AU  - Li, n 
AU  - Chen, Si 
AU  - Sun, Wengang 
AU  - Hu, Xiaoqing 

TI  - A Rare Long Term Survival Case of Complete Pentalogy of Cantrell in Adult after One-Staged Surgery
T2  - Structural and Congenital Heart Disease

PY  - 2021
VL  - 16
IS  - 5
SN  - 3071-1738

AB  - Pentalogy of Cantrell is a rare congenital abnormality. Even with high-quality medical care and staged corrective surgeries in professional hospitals, the mortality rate is still very high and long-term prognosis is poor. Survival is largely determined by the complexity and severity of cardiac abnormalities, the efficiency of abdominal wall closure and postoperative complications. A 24-year-old male patient with complete pentalogy of Cantrell was diagnosed. One-stage surgical repair of all abnormalities were completed. The patient recovered well and had been follow-up for 7 years. He has a good cosmetic outcome, with no signs of cardiac dysfunction. No complications were noted.
KW  - Pentalogy of cantrell; adult; one-stage surgery

DO  - 10.32604/CHD.2021.015749