TY  - EJOU
AU  - Luo, Kai 
AU  - Zheng, Jinghao 
AU  - Pan, Yanjun 
AU  - Zhu, Zhongqun 
AU  - He, Xiaomin 
AU  - Zhang, Hao 

TI  - One-and-a-Half Ventricle Repair with Hemi-Mustard/Bidirectional Glenn/Rastelli Procedure in a Patient with Double Outlet Right Ventricle and Atrioventricular Discordance: A Case Report
T2  - Structural and Congenital Heart Disease

PY  - 2026
VL  - 21
IS  - 2
SN  - 3071-1738

AB  - Background Double outlet right ventricle (DORV) is a complex congenital heart disease with significant anatomical variations. Patients with atrioventricular discordance have traditionally been managed with univentricular palliation strategies. However, advances in surgical concepts and techniques have enabled biventricular or one-and-a-half ventricle repair in selected patients, even after prior palliation. Case presentation We report a case of a 32-year-old woman with DORV and atrioventricular discordance who successfully underwent conversion to a one-and-a-half ventricle circulation using a combined Hemi-Mustard/Rastelli procedure with preservation of a pre-existing bidirectional Glenn shunt, performed 18 years after initial palliation. Conclusion This case provides insight into the surgical decision-making and technical considerations for managing similarly complex congenital anomalies.
KW  - Hemi-mustard/bidirectional Glenn/Rastelli procedure; double outlet right ventricle with atrioventricular discordance; post-palliation; one-and-a-half ventricle repair

DO  - 10.32604/schd.2026.078290