Home / Journals / CHD / Vol.16, No.2, 2021
  • Open Access

    ARTICLE

    3.0T MR Coronary Angiography after Arterial Switch Operation for Transposition of The Great Arteries—Gd-FLASH Versus Non-Enhanced SSFP. A Feasibility Study

    Kathrine Rydén Suther1,*, Charlotte de Lange1,2, Henrik Brun3, Rolf Svendsmark1, Bac Nguyen1, Stig Larsen4, Bjarne Smevik1, Arnt Eltvedt Fiane5,6, Harald Lauritz Lindberg6, Einar Hopp1
    Congenital Heart Disease, Vol.16, No.2, pp. 107-121, 2021, DOI:10.32604/CHD.2021.014164
    Abstract Background: Patency of the coronary arteries is an issue after reports of sudden cardiac death in patients with transposition of the great arteries (TGA) operated with arterial switch (ASO). Recent studies give rise to concern regarding the use of ionising radiation in congenital heart disease, and assessment of the coronary arteries with coronary MR angiography (CMRA) might be an attractive non-invasive, non-ionising imaging alternative in these patients. Theoretically, the use of 3.0T CMRA should improve the visualisation of the coronary arteries. The objective of this study was to assess feasibility of 3.0T CMRA at the coronary artery origins by comparing… More >

  • Open Access

    ARTICLE

    Effect of Hemodilution on Fluctuation of Cerebral Oxygen Saturation during Cardiopulmonary Bypass in Children with Cyanotic Congenital Heart Disease

    Misook Seo1, In-Kyung Song2, Hye-Mee Kwon2, Byungdoo Andrew Lee2, Won-Jung Shin2,*
    Congenital Heart Disease, Vol.16, No.2, pp. 123-136, 2021, DOI:10.32604/CHD.2021.012626
    Abstract Background: In patients with cyanotic congenital heart disease (CHD), cerebral oxygenation may be maintained by elevations in hematocrit (Hct). Hemodilution accompanying cardiopulmonary bypass (CPB), however, can disrupt cerebral oxygen balance, leading to fluctuations in cerebral oxygen saturation (ScO2). The present study investigated the effects of Hct changes on the fluctuation of ScO2 during CPB in cyanotic CHD using performance measurement (PM). Methods: Children with CHD (51 acyanotic and 46 cyanotic) who had undergone cardiac surgery using CPB were enrolled. Median performance error (MDPE), median absolute performance error (MDAPE), and wobble parameters of ScO2 were calculated before (reference value), during, and… More >

  • Open Access

    CASE REPORT

    Successful Vaginal Delivery after Implantable Cardiac Defibrillator Placement for Management of Ventricular Tachycardia

    Sara Moufarrij1, Manisha Gandhi1, Wilson Lam2, Angeline Opina2,*
    Congenital Heart Disease, Vol.16, No.2, pp. 137-139, 2021, DOI:10.32604/CHD.2021.013165
    Abstract A 23-year-old female with Tetralogy of Fallot who is 30w6d pregnant presented with palpitations and syncope from an outside hospital. She was found to have ventricular tachycardia. Successful placement of a transvenous implantable cardiac defibrillator allowed for symptomatic control and a subsequent successful vaginal delivery. More >

  • Open Access

    ARTICLE

    High-Risk Congenital Coronary Abnormalities in Patients with Bicuspid Aortic Valve

    Félix Collard1, Dimitrios Buklas2, Pascale Maragnes1, Fabien Labombarda1,*
    Congenital Heart Disease, Vol.16, No.2, pp. 141-146, 2021, DOI:10.32604/CHD.2021.013180
    Abstract Objective: Abnormal coronary artery origin (ACAO) from the opposite sinus with inter-arterial course of the ectopic proximal vessel is associated with the greatest potential for clinical manifestations, specifically sudden death. Data remain limited regarding the association between bicuspid aortic valve (BAV) and this potentially dangerous coronary variant reported in up to 0.6% in the general population. We investigated the frequency of this high-risk ACAO with inter-arterial course in our surgical series of BAV patients. Methods and Results: We conducted a retrospective study to identify BAV patients with ACAO and inter-arterial course who underwent elective aortic valve/root surgery between 2010 and… More >

  • Open Access

    CASE REPORT

    Transcatheter Closure of a Right Pulmonary Artery to Left Atrium Fistula Using a Ventricular Septal Defect Occluder

    Diqi Zhu1, Xiaohong Gu2, Jie Shen1,*, Fen Li1,*
    Congenital Heart Disease, Vol.16, No.2, pp. 147-150, 2021, DOI:10.32604/CHD.2021.014360
    Abstract Background: Communication between the right pulmonary artery (RPA) and left atrium (LA) is a rare cause of central cyanosis in pediatric patients. Case presentation: We describe a 3-year-old female patient with an oxygen saturation of 70% at admission. The echocardiogram indicated an abnormal color flow Doppler in the LA and she underwent standard cardiac catheterization. The angiography of pulmonary artery revealed a 7.4 mm × 7.6 mm fistula between the RPA and LA and achieved successful closure using ventricular septal defect occlusion. Conclusion: The fistula between pulmonary artery and left atrium is an extremely rare but treatable congenital defect. It… More >

  • Open Access

    ARTICLE

    Transcatheter Closure of Perimembranous Ventricular Septal Defect Using the Amplatzer Duct Occluder II

    Hongxiao Sun, Gang Luo, Zhanhui Du, Zhixian Ji, Silin Pan*
    Congenital Heart Disease, Vol.16, No.2, pp. 151-157, 2021, DOI:10.32604/CHD.2021.014770
    Abstract Objective: To evaluate the efficacy of Amplatzer duct occluder II (ADO II) in the treatment of perimembranous ventricular septal defect (pmVSD) in children. Methods: Between June 2017 and June 2020, 13 patients with pmVSD had attempted transcatheter closure using ADO II, seven of patients were used antegrade approach and six of them were used retrograde approach. Results: There were 8 males and 5 females, age from 1 to 7 years, weight from 10.5 to 31.0 kg, and VSD size from 2.0 to 4.0 mm. Procedure was successful in all cases with the outer diameter of the occluders ranging from 4… More >

  • Open Access

    ARTICLE

    Screening Coarctation of Aorta with Clinical and Echocardiographic Profiles in Infants: A Pilot Study

    Ruikun Zou1, Yifei Wang1,*, Chengcheng Pang2, Yunxia Sun1, Chen Chen1, Jian Zhuang3
    Congenital Heart Disease, Vol.16, No.2, pp. 159-170, 2021, DOI:10.32604/CHD.2021.015050
    Abstract Aim: To determine the profiles of clinical features including four-limb blood pressure (BP), saturations of peripheral oxygen (SpO2), and echocardiographic features in infants with coarctation of aorta (CoA) to facilitate congenital heart diseases screening. Methods: The charts of infants with CoA were retrospectively reviewed. All in-hospital infants suspected of congenital heart diseases by clinical teams were prospectively measured of four limbs BPs and SpO2 in a regional cardiac transferring center during 2013 and 2019. Echocardiography as a gold standard test was followed within 2 days after suspicion. All infants were divided into non-significant CoA group or significant CoA group based… More >

  • Open Access

    ARTICLE

    Kabuki-Syndrome and Congenital Heart Disease—A Twenty-Year Institutional Experience

    Reghan Conrey1,*, Sebastian Tume2, Carlos Bonilla-Ramirez3, Seema Lalani4, Dean McKenzie3,#, Marc Anders2,#
    Congenital Heart Disease, Vol.16, No.2, pp. 171-181, 2021, DOI:10.32604/CHD.2021.014409
    Abstract Background: Patients with genetic syndromes who undergo surgery to correct congenital heart defects can be at risk for increased morbidity or mortality. Surgical outcomes and postoperative courses following congenital heart surgery in patients with Kabuki-Syndrome (KS) have not been well studied. Objectives: The purpose of this study was to describe the postoperative courses and associated outcomes in the largest set of KS patients undergoing congenital heart surgery to date. Methods: Patients with a confirmed molecular diagnosis of KS and a diagnosis of a CHD admitted to Texas Children’s Hospital between January 1, 2000 and January 1, 2020 were included (n… More >

  • Open Access

    CASE REPORT

    The ASD that Wouldn’t Go Away: An Unusual Case of ASD Device Failure in a Patient with Marfan Syndrome

    Christopher M. Day1,*, Neda Mulla2, Timothy Martens3, Brent M. Gordon2
    Congenital Heart Disease, Vol.16, No.2, pp. 183-187, 2021, DOI:10.32604/CHD.2021.014337
    Abstract Marfan syndrome patients have connective tissue abnormalities that predispose them to intracardiac defects and postoperative complications. We present a case of late onset ASD device failure secondary to device movement within the atrial septum in a girl with Marfan syndrome. This case study suggests that further studies are necessary to determine the optimal device and approach for ASD repair in this patient cohort. More >

  • Open Access

    REVIEW

    Important Newborn Cardiac Diagnostic Dilemmas for the Neonatologist and Cardiologist–A Clinical Perspective

    Samuel Menahem1,2,*, Arvind Sehgal3,4
    Congenital Heart Disease, Vol.16, No.2, pp. 189-196, 2021, DOI:10.32604/CHD.2021.014903
    Abstract Most congenital heart disease (CHD) is readily recognisable in the newborn. Forewarned by previous fetal scanning, the presence of a murmur, tachypnoea, cyanosis and/or differential pulses and saturations all point to a cardiac abnormality. Yet serious heart disease may be missed on a fetal scan. There may be no murmur or clinical cyanosis, and tachypneoa may be attributed to non-cardiac causes. Tachypnoea on day 1 is usually non-cardiac except arising from ventricular failure or a large systemic arteriovenous fistula. A patent ductus arteriosus (PDA) may support either pulmonary or systemic duct dependent circulations. The initially high pulmonary vascular resistance (PVR)… More >

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