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Giant-Size Main Pulmonary Artery Aneurysm in an Adult Patient with Ebstein Anomaly and Dextrocardia

Kristina Krzelj1,#,*, Irena Ivanac Vranesic2,#, Kristina Maric Besic2, Zeljko Duric1, Darko Anic1

1 Department of Cardiac Surgery, University Hospital Centre Zagreb, Zagreb, Croatia
2 Department of Cardiovascular Diseases, University Hospital Centre Zagreb, Zagreb, Croatia

* Corresponding Author: Kristina Krzelj. Email: email

(This article belongs to this Special Issue: Nightmare Case Reports in Congenital Heart Disease)

Congenital Heart Disease 2023, 18(2), 207-212. https://doi.org/10.32604/chd.2023.027453

Abstract

Main pulmonary artery aneurysms are rare, mostly asymptomatic and discovered accidentally. The main pulmonary artery aneurysms may be idiopathic or secondary to underlying diseases such as pulmonary hypertension, Behcet’s disease, connective tissue disorders, congenital heart disease, vasculitis, syphilis, tuberculosis and endocarditis. There are some indices that dextrocardia is associated with anomalies of the pulmonary arteries and pulmonary valve. A rare occurrence of main pulmonary artery aneurysms results in a lack of recommendations, so the remaining challenges are whether main pulmonary artery aneurysms should be treated, how, and when. The decision on surgical intervention or conservative treatment of the main pulmonary artery aneurysms depends on its size, etiology and accompanying diseases and includes a multidisciplinary heart team. Our case of the main pulmonary artery aneurysm and pulmonary valve abnormality associated with Ebstein anomaly and dextrocardia in a 67-year-old male patient brings causality considerations and treatment options in such a unique condition.

Graphical Abstract

Giant-Size Main Pulmonary Artery Aneurysm in an Adult Patient with Ebstein Anomaly and Dextrocardia

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Cite This Article

Krzelj, K., Vranesic, I. I., Besic, K. M., Duric, Z., Anic, D. (2023). Giant-Size Main Pulmonary Artery Aneurysm in an Adult Patient with Ebstein Anomaly and Dextrocardia. Congenital Heart Disease, 18(2), 207–212.



cc This work is licensed under a Creative Commons Attribution 4.0 International License , which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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