Open Access

CASE REPORT

Upper pole multicystic dysplasia and ureteropelvic junction obstruction associated with obstructive-refl uxing megaureter in a neonate with a single kidney

Endre Z. Neulander, Tiberiu Katz, Jacob Kaneti

Department of Urology, Division of Surgery, Soroka University Medical Center, Ben Gurion University, Beer Sheva, Israel
Address correspondence to Dr. Endre Z. Neulander, Department of Urology, Ben Gurion University, PO Box 151, Beer Sheva, Israel 84101

Canadian Journal of Urology 2010, 17(6), 5472-5474.

Abstract

A 20-day-old male neonate presented with fever and hydronephrosis. Evaluation revealed that the patient had a single left kidney and a rare combination of multiple congenital malformations: upper pole segmental multicystic dysplasia, ureteropelvic junction obstruction, and an obstructive and refl uxing megaureter (ureterovesical junction obstruction). We performed percutaneous drainage of the infected and obstructed upper collecting system and then used a sequential approach to manage the patient’s anomalies. First, we performed an upper pole partial nephrectomy and pyeloplasty with a modifi ed Y ureterostomy. Second, when the child was older, we performed ureterovesical reimplantation with ureteral tailoring. Currently, after 5 years of follow up, the patient has stable renal function.

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