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RESIDENT’S CORNER
Giant renal angiomyolipoma in a solitary kidney
Ericka Sohlberg, Andrew Sun, Rustin Massoudi, Kris Prado, Eila Skinner
Department of Urology, Stanford University, Stanford, California, USA
Address correspondence to Dr. Ericka Sohlberg, 300 Pasteur
Drive, Grant Building S285, Stanford, CA 94305 USA
Canadian Journal of Urology 2018, 25(6), 9614-9616.
Abstract
While renal angiomyolipomas (AMLs) generally remain
small and asymptomatic, larger AMLs are more common in
tuberous sclerosis patients. Giant AMLs over 20 cm are a
rare entity and little is known about their management. We
present a unique case of a 48-year-old woman with tuberous sclerosis and a 39 cm AML arising from a solitary kidney,
after undergoing nephrectomy for a prior AML. Giant renal
AMLs can occur in patients with tuberous sclerosis and
resection should be considered even for large tumors. Renal
sparing is often difficult and patients should be counseled
about potential need for postoperative hemodialysis.
Keywords
AML, giant angiomyolipoma, tuberous sclerosis
Cite This Article
APA Style
Sohlberg, E., Sun, A., Massoudi, R., Prado, K., Skinner, E. (2018). Giant renal angiomyolipoma in a solitary kidney. Canadian Journal of Urology, 25(6), 9614–9616.
Vancouver Style
Sohlberg E, Sun A, Massoudi R, Prado K, Skinner E. Giant renal angiomyolipoma in a solitary kidney. Can J Urology. 2018;25(6):9614–9616.
IEEE Style
E. Sohlberg, A. Sun, R. Massoudi, K. Prado, and E. Skinner, “Giant renal angiomyolipoma in a solitary kidney,” Can. J. Urology, vol. 25, no. 6, pp. 9614–9616, 2018.
Copyright © 2018 The Canadian Journal of Urology.