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Right aortic arch with situs solitus

William N. Evans1,2, Ruben J. Acherman1,2, Dean Berthoty3, Gary A. Mayman1,2, Michael L. Ciccolo1,4, Sergio A. Carrillo1,4, Humberto Restrepo1,2

1 Children’s Heart Center Nevada, Las Vegas, Nevada, USA
2 Division of Pediatric Cardiology, Department of Pediatrics, University of Nevada Las Vegas, School of Medicine, Las Vegas, Nevada, USA
3 Red Rock Radiology, Las Vegas, Nevada, USA
4 Department of Surgery, University of Nevada Las Vegas, School of Medicine, Las Vegas, Nevada, USA

* Corresponding Author: William N Evans, MD, Children’s Heart Center Nevada, 3006 S Maryland Parkway Ste 690, Las Vegas, NV 89109. Email: email

Congenital Heart Disease 2018, 13(4), 624-627.


Patients: We reviewed all patients evaluated at our center with situs solitus, levocardia, and a right aortic arch that were born between January 2000 and January 2018. Results: From our databases, we identified 204 patients. We excluded patients with a double aortic arch from analysis. Of the 204 patients, 103 (50%) were male. Of the 204 patients, 95 (47%) had an isolated right aortic arch. Of the 95 with an isolated right aortic arch, 4 (4%) had chromosome 22q11.2 deletion syndrome, and 89 (94%) had a vascular ring. Of the 204 patients, 109 (53%) had a surgical intracardiac malformation. Of the 109, with an associated surgical intracardiac malformation, 38 (35%) had chromosome 22q11.2 deletion syndrome, and 28 (26%) had a vascular ring. Overall, of the 204 patients, 200 (98%) had a vascular ring, an associated intracardiac malformation, or both. Prenatal detection was 85% (40/47) for the subset of patients born in Southern Nevada between January 2015 and January 2018. Conclusion: this review, to best of our knowledge, reports one of largest series of right aortic arches in the literature. Data from our cohort demonstrates that a right aortic arch in situs solitus is almost always associated with pathology. Further, our center’s right aortic arch prenatal detection rate exceeds previous reports.


Cite This Article

APA Style
Evans, W.N., Acherman, R.J., Berthoty, D., Mayman, G.A., Ciccolo, M.L. et al. (2018). Right aortic arch with situs solitus. Congenital Heart Disease, 13(4), 624-627.
Vancouver Style
Evans WN, Acherman RJ, Berthoty D, Mayman GA, Ciccolo ML, Carrillo SA, et al. Right aortic arch with situs solitus. Congeni Heart Dis. 2018;13(4):624-627
IEEE Style
W.N. Evans et al., "Right aortic arch with situs solitus," Congeni. Heart Dis., vol. 13, no. 4, pp. 624-627. 2018.

cc This work is licensed under a Creative Commons Attribution 4.0 International License , which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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