Open Access
ARTICLE
Right aortic arch with situs solitus
William N. Evans1,2, Ruben J. Acherman1,2, Dean Berthoty3, Gary A. Mayman1,2, Michael L. Ciccolo1,4, Sergio A. Carrillo1,4, Humberto Restrepo1,2
1 Children’s Heart Center Nevada, Las Vegas, Nevada, USA
2 Division of Pediatric Cardiology,
Department of Pediatrics, University of
Nevada Las Vegas, School of Medicine, Las
Vegas, Nevada, USA
3 Red Rock Radiology, Las Vegas, Nevada,
USA
4 Department of Surgery, University of
Nevada Las Vegas, School of Medicine, Las
Vegas, Nevada, USA
* Corresponding Author: William N Evans, MD, Children’s Heart Center Nevada, 3006 S Maryland Parkway Ste 690, Las Vegas, NV 89109. Email:
Congenital Heart Disease 2018, 13(4), 624-627. https://doi.org/10.1111/chd.12623
Abstract
Patients: We reviewed all patients evaluated at our center with situs solitus, levocardia, and a right
aortic arch that were born between January 2000 and January 2018.
Results: From our databases,
we identified 204 patients. We excluded patients with a double aortic arch from analysis. Of the
204 patients, 103 (50%) were male. Of the 204 patients, 95 (47%) had an isolated right aortic arch.
Of the 95 with an isolated right aortic arch, 4 (4%) had chromosome 22q11.2 deletion syndrome,
and 89 (94%) had a vascular ring. Of the 204 patients, 109 (53%) had a surgical intracardiac malformation. Of the 109, with an associated surgical intracardiac malformation, 38 (35%) had
chromosome 22q11.2 deletion syndrome, and 28 (26%) had a vascular ring. Overall, of the 204
patients, 200 (98%) had a vascular ring, an associated intracardiac malformation, or both. Prenatal
detection was 85% (40/47) for the subset of patients born in Southern Nevada between January
2015 and January 2018.
Conclusion: this review, to best of our knowledge, reports one of largest
series of right aortic arches in the literature. Data from our cohort demonstrates that a right aortic
arch in situs solitus is almost always associated with pathology. Further, our center’s right aortic
arch prenatal detection rate exceeds previous reports.
Keywords
Cite This Article
Evans, W. N., Acherman, R. J., Berthoty, D., Mayman, G. A., Ciccolo, M. L. et al. (2018). Right aortic arch with situs solitus.
Congenital Heart Disease, 13(4), 624–627.