Open Access

RESIDENT’S CORNER

Implications of Erdheim-Chester disease and percutaneous renal access

Lael Stieglitz, Vernon M. Pais Jr.

Department of Surgery, Section of Urology, Dartmouth Hitchcock Medical Center, Lebanon, New Hampshire, USA
Address correspondence to Dr. Vernon M. Pais Jr., Department of Surgery, Section of Urology, Dartmouth Hitchcock Medical Center, 1 Medical Center Drive, Lebanon, NH 03756 USA

Canadian Journal of Urology 2020, 27(6), 10493-10495.

Abstract

Erdheim-Chester disease (ECD) is a rare systemic histiocytosis with urologic manifestations in a majority of affected patients. An important manifestation is a pronounced retroperitoneal fibrosis with reported dense inflammatory rind surrounding the kidneys. We report a case of a patient with large stone burden necessitating percutaneous nephrolithotomy and the implications related to his Erdheim-Chester-related retroperitoneal fibrotic changes. Foreknowledge of these implications may inform perioperative counseling and surgical planning to maximize opportunity for successful outcomes.

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