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Right aortic arch with situs solitus frequently heralds a vascular ring

William N. Evans1,2, Ruben J. Acherman1,2, Michael L. Ciccolo1,3, Sergio A. Carrillo1,3, Gary A. Mayman1,2, Carlos F. Luna1,2, Robert C. Rollins1,2, William J. Castillo1,2, Alvaro Galindo1,2, Abraham Rothman1,2, John A. Alexander1,2, Tina W. Kwan1,2, Humberto Restrepo1,2
1 Children’s Heart Center Nevada, Las Vegas, Nevada
2 Division of Pediatric Cardiology, Department of Pediatrics, University of Nevada School of Medicine, Las Vegas, Nevada
3 Department of Surgery, University of Nevada School of Medicine, Las Vegas, Nevada
* Corresponding Author: William N. Evans, Children’s Heart Center Nevada, 3006 S. Maryland Parkway Ste. 690, Las Vegas, NV. Email:

Congenital Heart Disease 2017, 12(5), 583-587. https://doi.org/10.1111/chd.12487

Abstract

Objective: We hypothesized that a right aortic arch in situs solitus, with or without an associated cardiovascular malformation, is often associated with a vascular ring.
Methods: From those born in Southern Nevada between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live births) with a right aortic arch and situs solitus. From the 50 patients, 6 did not meet inclusion criteria for further analysis.
Results: Of the 44 remaining, 33 (75%) had a vascular ring. Of the 33 with a vascular ring, 26 (79%) occurred with an isolated right aortic arch, and 7 (21%) had an associated cardiovascular malformation. Of the total 44 patients with a right aortic arch in situs solitus, 34 (79%) were diagnosed prenatally.
Conclusions: In conclusion, we found a right aortic arch in situs solitus was often associated with a vascular ring. Further, to the best of our knowledge, no previous general population study has demonstrated an equal or higher right aortic arch, prenatal detection rate of 79%.

Keywords

prenatal diagnosis, right aortic arch, vascular ring

Cite This Article

Evans, W. N., Acherman, R. J., Ciccolo, M. L., Carrillo, S. A., Mayman, G. A. et al. (2017). Right aortic arch with situs solitus frequently heralds a vascular ring. Congenital Heart Disease, 12(5), 583–587.



This work is licensed under a Creative Commons Attribution 4.0 International License , which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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