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Scimitar Syndrome: Role of Right Atrial Longitudinal Strain. A Case Report

Isabella Leo1, Jolanda Sabatino1,2,3, Sabrina La Bella1, Antonio Strangio1, Iolanda Aquila1, Concetta Procopio1, Carmen Anna Maria Spaccarotella1, Maria Petullà4, Salvatore De Rosa1,2, Ciro Indolfi1,2,5,*

1 Division of Cardiology, Department of Medical and Surgical Sciences, Magna Graecia University, Catanzaro, Italy
2 Cardiovascular Research Center, Magna Graecia University, Catanzaro, Italy
3 Department of Paediatric Cardiology, Royal Brompton Hospital, London, UK
4 Department of Radiology, Magna Graecia University, Catanzaro, Italy
5 Mediterranea Cardiocentro, Napoli, Italy

* Corresponding Author: Ciro Indolfi. Email:

Congenital Heart Disease 2021, 16(4), 411-416.


We describe a case of a rare congenital heart disorder, scimitar syndrome, diagnosed in an adult woman presenting with dyspnea on exertion, chest pain and recurrent episodes of pulmonary infections. The hallmark of the syndrome is the presence of an enlarged anomalous pulmonary vein draining into the inferior vena cava. Speckle tracking echocardiography, including the often-forgotten atrial strain evaluation, is a sensitive parameter that should be routinely used for a better clinical and prognostic evaluation of patients with congenital heart disease (CHD).


Cite This Article

Leo, I., Sabatino, J., Bella, S. L., Strangio, A., Aquila, I. et al. (2021). Scimitar Syndrome: Role of Right Atrial Longitudinal Strain. A Case Report. Congenital Heart Disease, 16(4), 411–416.

This work is licensed under a Creative Commons Attribution 4.0 International License , which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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