Open Access

CASE REPORT

A Rare Case of Concordant Atrioventricular Connection to L-Looped Ventricles in Situs Solitus: 4-Dimensional Magnetic Resonance Imaging and 3D Printing

Gregory Perens^1,*, Takegawa Yoshida², J. Paul Finn²

1 UCLA Mattel Children’s Hospital, Children’s Heart Center, Los Angeles, CA, USA
2 Diagnostic Cardiovascular Imaging Laboratory, Department of Radiology, 12222 David Geffen School of Medicine at UCLA, Los Angeles, CA, USA

* Corresponding Author: Gregory Perens. Email:

Congenital Heart Disease 2022, 17(4), 387-392. https://doi.org/10.32604/chd.2022.021233

Received 05 February 2022; Accepted 24 May 2022; Issue published 04 July 2022

Abstract

An infant male presented with the rare anatomy consisting of situs solitus, concordant atrioventricular connections to L-looped ventricles, double outlet right ventricle (DORV), and hypoplastic aortic arch. 6 months after neonatal aortic arch repair, the morphologic right ventricle function deteriorated, and surgical evaluation was undertaken to determine if either biventricular repair with a systemic morphologic left ventricle or right ventricular exclusion was possible. After initial echocardiography, magnetic resonance imaging (MRI) was used to create detailed axial and 4-dimensional (4D) images and 3-dimensional (3D) printed models. The detailed anatomy of this rare, complex case and its use in pre-surgical planning is presented.

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Graphical Abstract

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Keywords

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