Christopher R. Broda, Katherine B. Salciccioli, Keila N. Lopez, Peter R. Ermis, Douglas S. Moodie, Heather A. Dickerson
Congenital Heart Disease, Vol.14, No.6, pp. 885-894, 2019, DOI:10.1111/chd.12856
Abstract Background: Heterotaxy syndrome (HS) is a condition in which the thoracoabdominal
organs demonstrate an abnormal lateral arrangement and is often associated with con‐
genital heart disease (CHD). Little is known about the adult HS population with CHD.
Objective: To describe the outcomes and sociodemographics of the adult CHD popu‐
lation with HS.
Methods: Records of patients 18 years of age or older with diagnoses of both CHD
and HS at Texas Children's Hospital from 1964 to 2018 were reviewed.
Results: Sixty‐two patients metinclusion criteria.Median agewas 22.7 [IQR19.6‐30.0]
years; 26 (42%) were female; and 13 (21%) of patients had a gap… More >