Open Access

CASE REPORT

One-and-a-Half Ventricle Repair with Hemi-Mustard/Bidirectional Glenn/Rastelli Procedure in a Patient with Double Outlet Right Ventricle and Atrioventricular Discordance: A Case Report

Kai Luo^#, Jinghao Zheng^#, Yanjun Pan, Zhongqun Zhu, Xiaomin He^*, Hao Zhang^*

Department of Cardiothoracic Surgery, Shanghai Children’s Medical Center, School of Medicine, Shanghai Jiao Tong University, National Children’s Medical Center, Shanghai, China

* Corresponding Authors: Xiaomin He. Email: ; Hao Zhang. Email:
# These authors contributed equally to this work

(This article belongs to the Special Issue: Special Issue from the 5^th Asian Association for Pediatric and Congenital Heart Surgery (AAPCHS) Annual Conference)

Structural and Congenital Heart Disease 2026, 21(2), 7 https://doi.org/10.32604/schd.2026.078290

Received 28 December 2025; Accepted 21 April 2026; Issue published 11 June 2026

Abstract

Background Double outlet right ventricle (DORV) is a complex congenital heart disease with significant anatomical variations. Patients with atrioventricular discordance have traditionally been managed with univentricular palliation strategies. However, advances in surgical concepts and techniques have enabled biventricular or one-and-a-half ventricle repair in selected patients, even after prior palliation. Case presentation We report a case of a 32-year-old woman with DORV and atrioventricular discordance who successfully underwent conversion to a one-and-a-half ventricle circulation using a combined Hemi-Mustard/Rastelli procedure with preservation of a pre-existing bidirectional Glenn shunt, performed 18 years after initial palliation. Conclusion This case provides insight into the surgical decision-making and technical considerations for managing similarly complex congenital anomalies.

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Keywords

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