Open Access

CASE REPORT

Transcatheter Closure of a Right Pulmonary Artery to Left Atrium Fistula Using a Ventricular Septal Defect Occluder

Diqi Zhu¹, Xiaohong Gu², Jie Shen^1,*, Fen Li^1,*

1 Department of Pediatric Cardiology, Shanghai Children’s Medical Center Affiliated to Shanghai Jiaotong University School of Medicine, Shanghai, 200127, China
2 Department of Radiology Shanghai Children’s Medical Center Affiliated to Shanghai Jiaotong University School of Medicine, Shanghai, 200127, China

* Corresponding Authors: Jie Shen. Email: ; Fen Li. Email:

Congenital Heart Disease 2021, 16(2), 147-150. https://doi.org/10.32604/CHD.2021.014360

Received 22 September 2020; Accepted 17 November 2020; Issue published 26 January 2021

Abstract

Background: Communication between the right pulmonary artery (RPA) and left atrium (LA) is a rare cause of central cyanosis in pediatric patients. Case presentation: We describe a 3-year-old female patient with an oxygen saturation of 70% at admission. The echocardiogram indicated an abnormal color flow Doppler in the LA and she underwent standard cardiac catheterization. The angiography of pulmonary artery revealed a 7.4 mm × 7.6 mm fistula between the RPA and LA and achieved successful closure using ventricular septal defect occlusion. Conclusion: The fistula between pulmonary artery and left atrium is an extremely rare but treatable congenital defect. It should be considered in differential diagnosis of cyanosis in children.

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Keywords

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