Kristina Krzelj^1,#,*, Irena Ivanac Vranesic^2,#, Kristina Maric Besic², Zeljko Duric¹, Darko Anic¹

Congenital Heart Disease, Vol.18, No.2, pp. 207-212, 2023, DOI:10.32604/chd.2023.027453

Abstract Main pulmonary artery aneurysms are rare, mostly asymptomatic and discovered accidentally. The main pulmonary artery aneurysms may be idiopathic or secondary to underlying diseases such as pulmonary hypertension, Behcet’s disease, connective tissue disorders, congenital heart disease, vasculitis, syphilis, tuberculosis and endocarditis. There are some indices that dextrocardia is associated with anomalies of the pulmonary arteries and pulmonary valve. A rare occurrence of main pulmonary artery aneurysms results in a lack of recommendations, so the remaining challenges are whether main pulmonary artery aneurysms should be treated, how, and when. The decision on surgical intervention or conservative treatment of the main pulmonary… More > Graphic Abstract

Lianne M. Geerdink^1,2,*, Malindi van der Mheen^3,4, Gideon J. du Marchie Sarvaas⁵, Irene M. Kuipers⁶, Stefan Frerich⁷, Henriëtte ter Heide², Willem A. Helbing⁸, Zina Feijzic¹, Christian Schroer⁹, Chris L. de Korte¹⁰, Livia Kapusta^1,11, Chris M. Verhaak¹², Elisabeth M. W. J. Utens^3,4

Congenital Heart Disease, Vol.15, No.6, pp. 457-472, 2020, DOI:10.32604/CHD.2020.012994

Abstract Background: Due to the improved survival rates of children and adolescents with congenital heart disease (CHD), more attention is now being directed towards their health-related quality of life (HRQoL), emotional and behavioral problems. Ebstein anomaly (EA) is a rare CHD with a broad clinical spectrum. The aim of the current study is to evaluate self- and proxy-reported HRQoL and emotional and behavioral problems in children and adolescents with EA. Methods: In this cross-sectional, multicenter study, we included EA patients (aged 8–17 years), who underwent routine clinical assessments in Dutch university hospitals between May 2017 and March 2019. The Generic Pediatric… More >

Varisara Pornprasertchai, Chodchanok Vijarnsorn, Supaluck Kanjanauthai, Paweena Chungsomprasong, Prakul Chanthong, Kritvikrom Durongpisitkul, Jarupim Soongswang

Congenital Heart Disease, Vol.14, No.4, pp. 619-627, 2019, DOI:10.1111/chd.12759

Abstract Background: The increasing number of patients with Ebstein anomaly (EA) surviving into adulthood implies improvements in the treatments for the complex lesion. We revisited the clinical outcomes of patients with EA to demonstrate their “real world” survival.
Objectives: To identify the survival and predictors of mortality in patients with EA who underwent medical or surgical management in the present era.
Methods: All patients who had EA with atrioventricular concordance between 1994 and 2016 were retrospectively reviewed. Baseline characteristics, initial echocardio‐ graphic findings, treatments, and outcomes were explored. The survival analysis was performed at the end of 2017. A multivariate analysis… More >

Philip Wackel^1,2, Bryan Cannon^1,2, Joseph Dearani³, Kristen Sessions^1,2, Kimberly Holst³, Jonathan Johnson^1,2, Frank Cetta^1,2

Congenital Heart Disease, Vol.13, No.1, pp. 26-30, 2018, DOI:10.1111/chd.12566

Abstract Background: The increased incidence of preoperative and postoperative arrhythmia in Ebstein anomaly (EA) prompted some clinicians to perform an electrophysiology study (EPS) in all patients prior to surgery for EA. The cone repair (CR) is the current surgical option of choice for most young patients with EA but the effect of the CR on arrhythmia is not well established.
Objectives: To assess the burden of arrhythmia in young patients after CR and to assess the utility of selective preoperative EPS.
Materials and Methods: A retrospective review of all patients <21 years of age with EA who had a CR at… More >