Ling Sun^1,#, Chengcheng Pang^1,#, Xiaoyan Wang^2,#, Mingguo Xu³, Zhiwei Zhang^1,*, Shushui Wang^1,*

Congenital Heart Disease, Vol.17, No.2, pp. 201-214, 2022, DOI:10.32604/chd.2022.018453

Abstract Background: Partial anomalous pulmonary venous connection (PAPVC) is frequently associated with atrial septal defect (ASD), especially sinus venosus defect (SVD). Although Waggstaffe described the pathology of SVDs in 1868, the exact anatomic features and the nature of SVD remains controversial. SVDs with no posterior atrial rim were observed in recent years. However, no studies suggested that absence of the residual posterior atrial septal tissue might be the key feature of SVD. The aims of this study were to investigate if absence of posterior rim of atrial septum played a crucial role in patients with SVD. Methods: From January 2011 to… More >

Shi-Joon Yoo^1,2,*, Sanga Lee³, Regina de la Mora⁴, Ankavipar Saprungruang², Christoph Haller⁵, Lee N. Benson², Vladimiro Vida⁶, Alvise Guariento⁶, Christopher Z. Lam¹

Congenital Heart Disease, Vol.17, No.1, pp. 5-23, 2022, DOI:10.32604/CHD.2022.018728

Abstract Sinus venosus defects include two varieties, superior and inferior sinus venosus defects. The superior sinus venosus defect is characterized by abnormal communication between two closely related venoatrial structures: 1) the normally positioned superior vena cava-right atrium complex and 2) the right pulmonary vein-left atrium complex that is displaced leftward, forward and upward. Inferior sinus venosus defects primarily involve the inferior vena cava-right atrial junction while the right pulmonary vein-left atrial junction can also be affected. Because of the rarity and wide variation of the defects, the morphological characterization of sinus venosus defects is inconsistent among investigators and often inaccurate. Modern… More >